| nr |
titel |
auteur |
tijdschrift |
jaar |
jaarg. |
afl. |
pagina('s) |
type |
| 1 |
Abnormal glucose tolerance and lung function in children with cystic fibrosis. Comparing oral glucose tolerance test and continuous glucose monitoring
|
Elidottir, H
|
|
|
20 |
5 |
p. 779-784
|
artikel
|
| 2 |
A mutational approach to dissect the functional role of the putative CFTR “PTM-CODE”
|
D'Amore, Claudio
|
|
|
20 |
5 |
p. 891-894
|
artikel
|
| 3 |
Antisense oligonucleotide-based drug development for Cystic Fibrosis patients carrying the 3849+10 kb C-to-T splicing mutation
|
Oren, Yifat S.
|
|
|
20 |
5 |
p. 865-875
|
artikel
|
| 4 |
Aquagenic wrinkling in children under two years of age: Could this be a potential clinical referral tool for cystic fibrosis among non-screened populations?
|
Paul, Grace R.
|
|
|
20 |
5 |
p. e77-e83
|
artikel
|
| 5 |
A survey of the prevalence, management and outcome of infants with an inconclusive diagnosis following newborn bloodspot screening for cystic fibrosis (CRMS/CFSPID) in six Italian centres
|
Terlizzi, Vito
|
|
|
20 |
5 |
p. 828-834
|
artikel
|
| 6 |
Beneath the surface: assessing cystic fibrosis pulmonary infections in the era of highly effective modulator therapy
|
Waters, V
|
|
|
20 |
5 |
p. 723-724
|
artikel
|
| 7 |
Breast development in a 7 year old girl with CF treated with ivacaftor: An indication for personalized dosing?
|
Jeyaratnam, Joshena
|
|
|
20 |
5 |
p. e63-e66
|
artikel
|
| 8 |
Changes in fecal microbiota with CFTR modulator therapy: A pilot study
|
Pope, CE
|
|
|
20 |
5 |
p. 742-746
|
artikel
|
| 9 |
Clinical evaluation of an evidence-based method based on food characteristics to adjust pancreatic enzyme supplements dose in cystic fibrosis
|
Calvo-Lerma, Joaquim
|
|
|
20 |
5 |
p. e33-e39
|
artikel
|
| 10 |
Comparative meta-analysis of cystic fibrosis cell models suggests partial endothelial-to-mesenchymal transition
|
Treps, Lucas
|
|
|
20 |
5 |
p. 876-880
|
artikel
|
| 11 |
Continuous glucose monitoring in cystic fibrosis–Benefits, limitations, and opportunities
|
Chan, Christine L.
|
|
|
20 |
5 |
p. 725-726
|
artikel
|
| 12 |
Continuous glucose monitoring indices predict poor FEV1 recovery following cystic fibrosis pulmonary exacerbations
|
Pallin, Michael
|
|
|
20 |
5 |
p. 785-791
|
artikel
|
| 13 |
Defining key outcomes to evaluate performance of newborn screening programmes for cystic fibrosis
|
Munck, Anne
|
|
|
20 |
5 |
p. 820-823
|
artikel
|
| 14 |
Diagnosis of CF: An evolving and enduring challenge
|
Ren, Clement L.
|
|
|
20 |
5 |
p. 727-728
|
artikel
|
| 15 |
Editorial Board
|
|
|
|
20 |
5 |
p. ii
|
artikel
|
| 16 |
Elexacaftor co-potentiates the activity of F508del and gating mutants of CFTR
|
Veit, Guido
|
|
|
20 |
5 |
p. 895-898
|
artikel
|
| 17 |
Entry of cystic fibrosis transmembrane conductance potentiator ivacaftor into the developing brain and lung
|
Qiu, Fiona
|
|
|
20 |
5 |
p. 857-864
|
artikel
|
| 18 |
Extended-culture and culture-independent molecular analysis of the airway microbiota in cystic fibrosis following CFTR modulation with ivacaftor
|
Einarsson, Gisli G.
|
|
|
20 |
5 |
p. 747-753
|
artikel
|
| 19 |
Extracellular phosphate enhances the function of F508del-CFTR rescued by CFTR correctors
|
Saint-Criq, Vinciane
|
|
|
20 |
5 |
p. 843-850
|
artikel
|
| 20 |
Improving and standardizing protocols for cystic fibrosis routine microbiology
|
Papon, Nicolas
|
|
|
20 |
5 |
p. e67-e68
|
artikel
|
| 21 |
Influence of pre-diabetic and pancreatic exocrine states on pulmonary and nutritional status in adults with Cystic Fibrosis
|
Potter, Kathryn J.
|
|
|
20 |
5 |
p. 803-809
|
artikel
|
| 22 |
Limb muscle size and contractile function in adults with cystic fibrosis: A systematic review and meta-analysis
|
Wu, Kenneth
|
|
|
20 |
5 |
p. e53-e62
|
artikel
|
| 23 |
Lumacaftor/ivacaftor in people with cystic fibrosis with an A455E–CFTR mutation
|
Berkers, Gitte
|
|
|
20 |
5 |
p. 761-767
|
artikel
|
| 24 |
Meconium Ileus due to GUCY2C gene mutations in three unrelated South Indian families
|
Varkki, Sneha
|
|
|
20 |
5 |
p. e84-e86
|
artikel
|
| 25 |
Nasal high-flow therapy as an adjunct to exercise in patients with cystic fibrosis: A pilot feasibility trial
|
Spoletini, Giulia
|
|
|
20 |
5 |
p. e46-e52
|
artikel
|
| 26 |
News article
|
|
|
|
20 |
5 |
p. 721-722
|
artikel
|
| 27 |
Non-invasive ventilation is associated with long-term improvements in lung function and gas exchange in cystic fibrosis adults with hypercapnic respiratory failure
|
Wadsworth, LE
|
|
|
20 |
5 |
p. e40-e45
|
artikel
|
| 28 |
Normal pancreatic function and false-negative CF newborn screen in a child born to a mother taking CFTR modulator therapy during pregnancy
|
Fortner, Christopher N.
|
|
|
20 |
5 |
p. 835-836
|
artikel
|
| 29 |
Optical Measurements of Sweat for in Vivo Quantification of CFTR Function in Individual Sweat Glands
|
Treggiari, Davide
|
|
|
20 |
5 |
p. 824-827
|
artikel
|
| 30 |
Pharmacokinetic interactions between ivacaftor and cytochrome P450 3A4 inhibitors in people with cystic fibrosis and healthy controls
|
van der Meer, Renske
|
|
|
20 |
5 |
p. e72-e76
|
artikel
|
| 31 |
Pharmacokinetics of oral antimycobacterials and dosing guidance for Mycobacterium avium complex treatment in cystic fibrosis
|
Martiniano, Stacey L.
|
|
|
20 |
5 |
p. 772-778
|
artikel
|
| 32 |
Rapid cystic fibrosis lung-function decline and in-vitro CFTR modulation
|
Gecili, Emrah
|
|
|
20 |
5 |
p. e69-e71
|
artikel
|
| 33 |
Relationship between airway dysbiosis, inflammation and lung function in adults with cystic fibrosis
|
Frey, Dario L.
|
|
|
20 |
5 |
p. 754-760
|
artikel
|
| 34 |
Short-term effect of elexacaftor-tezacaftor-ivacaftor on lung function and transplant planning in cystic fibrosis patients with advanced lung disease
|
B, Bermingham
|
|
|
20 |
5 |
p. 768-771
|
artikel
|
| 35 |
SLC26A9 SNP rs7512462 is not associated with lung disease severity or lung function response to ivacaftor in cystic fibrosis patients with G551D-CFTR
|
Eastman, Alice C.
|
|
|
20 |
5 |
p. 851-856
|
artikel
|
| 36 |
The association between body composition, leptin levels and glucose dysregulation in youth with cystic fibrosis
|
Granados, Andrea
|
|
|
20 |
5 |
p. 796-802
|
artikel
|
| 37 |
The prevalence of aberrations in body composition in pediatric cystic fibrosis patients and relationships with pulmonary function, bone mineral density, and hospitalizations
|
Ritchie, Hannah
|
|
|
20 |
5 |
p. 837-842
|
artikel
|
| 38 |
Trends in nontuberculous mycobacteria infection in children and young people with cystic fibrosis
|
Abidin, Noreen Zainal
|
|
|
20 |
5 |
p. 737-741
|
artikel
|
| 39 |
Updated guidance on the management of children with cystic fibrosis transmembrane conductance regulator-related metabolic syndrome/cystic fibrosis screen positive, inconclusive diagnosis (CRMS/CFSPID)
|
Barben, Jürg
|
|
|
20 |
5 |
p. 810-819
|
artikel
|
| 40 |
Very early glucose tolerance abnormalities in children with cystic fibrosis
|
Blanquer, Marie
|
|
|
20 |
5 |
p. 792-795
|
artikel
|
| 41 |
VIP reduction in the pancreas of F508del homozygous CF mice and early signs of Cystic Fibrosis Related Diabetes (CFRD)
|
Semaniakou, Anna
|
|
|
20 |
5 |
p. 881-890
|
artikel
|
| 42 |
Vitamin D supplementation in patients with cystic fibrosis: A systematic review and meta-analysis
|
Juhász, Márk Félix
|
|
|
20 |
5 |
p. 729-736
|
artikel
|
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