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Fatal Propionic Acidemia in Mice Lacking Propionyl-CoA Carboxylase and Its Rescue by Postnatal, Liver-specific Supplementation via a Transgene* |
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Titel: |
Fatal Propionic Acidemia in Mice Lacking Propionyl-CoA Carboxylase and Its Rescue by Postnatal, Liver-specific Supplementation via a Transgene* |
Auteur: |
Miyazaki, Toru Ohura, Toshihiro Kobayashi, Makio Shigematsu, Yosuke Yamaguchi, Seiji Suzuki, Yoichi Hata, Ikue Aoki, Yoko Yang, Xue Minjares, Christina Haruta, Ikuko Uto, Hirofumi Ito, Yuriko Müller, Urs |
Verschenen in: |
The journal of biological chemistry |
Paginering: |
Jaargang 276 () nr. 38 pagina's 35995-35999 |
Jaar: |
2001 |
Inhoud: |
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Uitgever: |
© 2001 ASBMB. Currently published by Elsevier Inc; originally published by American Society for Biochemistry and Molecular Biology. |
Bronbestand: |
Elektronische Wetenschappelijke Tijdschriften |
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