The Chemical Chaperone, PBA, Reduces ER Stress and Autophagy and Increases Collagen IV α5 Expression in Cultured Fibroblasts From Men With X-Linked Alport Syndrome and Missense Mutations
Titel:
The Chemical Chaperone, PBA, Reduces ER Stress and Autophagy and Increases Collagen IV α5 Expression in Cultured Fibroblasts From Men With X-Linked Alport Syndrome and Missense Mutations
Auteur:
Wang, Dongmao Mohammad, Mardhiah Wang, Yanyan Tan, Rachel Murray, Lydia S. Ricardo, Sharon Dagher, Hayat van Agtmael, Tom Savige, Judy