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Mice harbouring a SCA28 patient mutation in AFG3L2 develop late-onset ataxia associated with enhanced mitochondrial proteotoxicity |
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Titel: |
Mice harbouring a SCA28 patient mutation in AFG3L2 develop late-onset ataxia associated with enhanced mitochondrial proteotoxicity |
Auteur: |
Mancini, Cecilia Hoxha, Eriola Iommarini, Luisa Brussino, Alessandro Richter, Uwe Montarolo, Francesca Cagnoli, Claudia Parolisi, Roberta Gondor Morosini, Diana Iulia Nicolò, Valentina Maltecca, Francesca Muratori, Luisa Ronchi, Giulia Geuna, Stefano Arnaboldi, Francesca Donetti, Elena Giorgio, Elisa Cavalieri, Simona Di Gregorio, Eleonora Pozzi, Elisa Ferrero, Marta Riberi, Evelise Casari, Giorgio Altruda, Fiorella Turco, Emilia Gasparre, Giuseppe Battersby, Brendan J. Porcelli, Anna Maria Ferrero, Enza Brusco, Alfredo Tempia, Filippo |
Verschenen in: |
Neurobiology of disease |
Paginering: |
Jaargang 124 () nr. C pagina's 14-28 |
Jaar: |
2019 |
Inhoud: |
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Uitgever: |
Elsevier Inc. |
Bronbestand: |
Elektronische Wetenschappelijke Tijdschriften |
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